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Vasculitides
Vasculitis disorders
| Question | Answer |
|---|---|
| Vasculitis | Inflammation and necrosis of blood vessels. |
| Polyarteritis nodosa (PAN) | Acute necrotizing vasculitis of medium-sized muscular arteries. Men and whites. Thrombosis/ischemia. Fibrinoid necrosis. Hep B serospositivity 30%. |
| Kawasaki Disease (mucocutaneous lymph node syndrome) | Acute necrotizing vasculitis. Infancy. Fever, rash, conjunctival lesions, oral lesions. Coronary aneurysms. Japan. Self-limiting. |
| Giant cell arteritis (temporal cell arteritis) | Focal. Granulomatous. Temporal artery, aorta. Old age females. Most common vasculitis. Nodular thickening/reduced lumen. Fragmentation of internal elastic lamina. Vision impairment. Polymyalgia rheumatica. |
| Hypersensitivity angiitis (microscopic polyangiitis, leukocytoclastic vasculitis) | Small vessels. Skin or systemic. Palpable purpura. Drugs, infections, tumors. Fibrinoid necrosis, extravasation of RBCs. p-ANCA. Glomerulonephritis/kidney failure. |
| Churg-Strauss syndrome | P-ANCA. Granulomatous. Eosinophilia. Systemic. Young people with asthma/allergies. |
| Takayasu arteritis. | Pulseless disease. Granulomatous thickening of aorta and large branches. Young Asian females. Panarteritis w/giant cells. Steroids/surgical reconstruction. |
| Thromboangiitis obliterans (Buerger disease) | Occlusive. Medium/small arteries. Distal arms/legs. Smokers. Middle-age men. Gangrene. Amputations. Intermittent claudication. |
| Wegener granulomatosis | Systemic necrotizing vasculitis. Granulomatous. Lungs, kidney, upper respiratory. Small vessels. Hematuria/proteinuria. Sinusitis/pneumonitis. C-ANCA. Cyclophosphamide. |